鼻腔血管球瘤：来自巴基斯坦的病例报告

文献信息

中文摘要

血管球瘤是罕见的良性间叶性肿瘤，起源于血管球体修饰的平滑肌细胞，主要见于远端肢体的甲下区域。累及鼻腔，尤其是以血管球瘤形式出现，极为罕见，仅限于病例报告。我们报告一例59岁男性，有长期鼻塞病史。临床和影像学评估显示一个血管性肿块，起源于右侧上颌窦并延伸至鼻腔。该病变经内镜下切除，术中见其异常富血供。组织病理学检查证实为血管球瘤。患者在四年随访期间无复发。鼻内血管球瘤极为罕见，可能模仿更常见的鼻腔病变。组织病理学和免疫组化对准确诊断至关重要。手术切除似乎可获得良好结局，复发主要归因于切除不彻底，但结论仍受该疾病罕见性的限制。

英文摘要

Glomus tumors are rare benign mesenchymal neoplasms arising from modified smooth muscle cells of the glomus body, primarily found in subungual regions of distal extremities. Involvement of the nasal cavity, particularly in the form of glomangiomas, is exceptionally rare and limited to case reports. We present a case of a 59-year-old male with a long-standing history of nasal obstruction. Clinical and radiological evaluations revealed a vascular mass originating from the right maxillary sinus and extending into the nasal cavity. The lesion was endoscopically excised and found intraoperatively to be unusually vascular. Histopathological examination confirmed the diagnosis of glomangioma. The patient has remained recurrence-free over four years of follow-up. Intranasal glomangiomas are exceptionally rare and may mimic more common nasal lesions. Histopathology and immunohistochemistry are crucial for accurate diagnosis. Surgical excision appears to offer favorable outcomes, with recurrence largely attributed to incomplete resection, though conclusions remain limited by the rarity of this entity.